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Impaired Binding to Junctophilin2 and Nanostructural Alteration in CPVT Mutation
liheng yin,
Alexandra Zahradnikova Jr,
Riccardo Rizzetto,
Simona Boncompagni,
Camille Rabesahala de Meritens,
YADAN ZHANG,
Pierre Joanne,
Elena Marques Sule,
Yuriana Aguilar-Torres,
Miguel Fernandez-Tenorio,
Olivier Villejoubert,
Linwei Li,
Yue Yi Wang,
Philippe Mateo,
Valerie Nicolas,
Pascale Gerbaud,
F Anthony Lai,
Romain Perrier,
Julio L Alvarez,
Ernst Niggli,
Héctor H Valdivia,
Carmen R Valdivia,
Josefina Ramos-Franco,
Esther Zorio,
Spyridon Zisimopoulos
,
Feliciano Protasi,
Jean-Pierre Benitah,
Ana-Maria Gomez
Circulation Research, Volume: 129, Issue: 3, Pages: e35 - e52
Swansea University Authors:
Camille Rabesahala de Meritens, YADAN ZHANG, Spyridon Zisimopoulos
DOI (Published version): 10.1161/circresaha.121.319094
Abstract
Impaired Binding to Junctophilin2 and Nanostructural Alteration in CPVT Mutation
Published in: | Circulation Research |
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ISSN: | 0009-7330 1524-4571 |
Published: |
Ovid Technologies (Wolters Kluwer Health)
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Online Access: |
Check full text
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URI: | https://cronfa.swan.ac.uk/Record/cronfa57636 |
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Keywords: |
mutation, ventricular tachycardia, calcium, junctophilin, ryanodine receptor, action potential |
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College: |
Faculty of Medicine, Health and Life Sciences |
Funders: |
British Heart Foundation (BHF) |
Issue: |
3 |
Start Page: |
e35 |
End Page: |
e52 |